Electronic ISSN 2287-0237

VOLUME

PRIMARY RENAL SYNOVIAL SARCOMA

SEPTEMBER 2015 - VOL.10 | CASE REPORT

Synovial sarcomas are tumors that often occur in the proximity of large joints of young adults and adolescents. Primary synovial sarcoma of the kidney is very rare and difficult to diagnose. To date, fewer than 50 cases of primary renal synovial sarcoma (SS) have been reported in literature published in English. There are no established guidelines regarding the management of this tumor given the limited number of cases reported. Although primary surgical resection is the treatment of choice for primary renal synovial sarcoma, the prognosis is poor with surgery alone. Here, we describe a case of a 25-year-old female with primary renal synovial sarcoma that was treated successfully by radical nephrectomy followed by adjuvant chemotherapy. Physicians should be aware of the possibility of malignancy in renal masses and raise the suspicion of synovial sarcoma, especially when patients with renal masses are young adults.

Keywords

synovial sarcoma, renal

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Figure 1: CT abdomen revealed 11.3x10.3x9.5 cm lobulated exophytic heterogeneous necrotic mass with contrast ensancment from anterior part and upper pole of left kidney.
Figure 2: Solid hemorrhagic globular tumor protruding from renal hilum with extensive hemorrhagic necrosis.
Figure 3: Monomorphic, plump short spindle cells growing in a solid sheet with indistinct cell borders. Mitosis is frequent. Tumors are positive for CD 99 and Bcl-2.
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